KMID : 0361020070500060552
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Korean Journal of Otolaryngology - Head and Neck Surgery 2007 Volume.50 No. 6 p.552 ~ p.555
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A Case of Basal Cell Nevus Syndrome with Odontogenic Keratocyst
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Park Shin-Hong
Kim Hyo-Yeol Kim Joon-Ho Hong Sa-Hyun
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Abstract
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Nevoid basal cell carcinoma syndrome (Gorlin syndrome) is a cancer predisposition syndrome characterized by multiple basal cell carcinomas and diverse developmental defects. Recently, we experienced a case of odontogenic keratocysts in a 13-year-old boy who was finally diagnosed as having nevoid basal cell carcinoma syndrome by genetic study. The purpose of this paper is to report odontogenic keratocyst as the first manifestation of nevoid basal cell carcinoma syndrome and to emphasize that one must consider this syndrome as a possible diagnosis in all cases of odontogenic keratocysts.
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KEYWORD
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Nevoid basal cell carcinoma syndrome, Odontogenic Keratocyst, Gorlin syndrome
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